Xeroderma Pigmentosum

Xeroderma Pigmentosum is a rare congenital and heredo-familial disorder showing undue sensitivity to light. The disorder starts in infancy, but may begin later in childhood or adult life.

Symptoms of Xeroderma Pigmentosum

The characteristic lesions are: hyperpigmentation, freckles and blotches, atrophic spots and telangiectasia. Later, warty growths, keratoses and epitheliomas may complicate the disorder. The exposed parts of the body are the sites of choice. Exposure to sunlight aggravates the condition, which may be accompanied by photophobia and keratitis.

Prognosis of Xeroderma Pigmentosum

The prognosis is bad in severe cases; patients die early, but some live to adulthood.

Treatment of Xeroderma Pigmentosum

The treatment administered is unsatisfactory. Patients should learn to live with their skins, respecting its undue sensitivity; they should avoid sunlight, and use anti-actinic creams. Keratoses and epitheliomata need surgical intervention; radio-therapy should be avoided in these cases. Dermabrasive surgery may be helpful in mild cases.

Corn and Callus

Bunion

Cracking

Maceration

Acrocyanosis

Livedo reticularis

Frost bite

Solar dermatitis

Xeroderma pigmentosum

Solar eczema

Solar urticaria

Actinic reticuloid